Ossifying fbromyxoid tumor (OFMT) is a rare soft tissue neoplasm of uncertain lineage and intermediate biological potential. It is more common in middle-aged men, usually arising from the deep tissues of the extremities. It is now established that it is a translocation related tumor, most often marked by translocation of PHF1 gene.
Surgery is the mainstay of treatment and proves usually curative, although, in rarer cases the disease shows malignant
features and tendency to recur both locally and at distant sites. In such cases, no standard treatment exists.

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• Response to isolated limb perfusion and chemotherapy with epirubicin plus ifosfamide in a metastatic malignant ossifying fbromyxoid tumor